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Orthodontic and orthognathic management of a patient with Apert syndrome: a case report.

Verdonck A, Bertrand J, Carels C, Swinnen S, Schoenaers J

University Hospitals of the KU Leuven, Leuven, Belgium. An.Verdonck@uz.kuleuven.ac.be

This case report describes the combined orthodontic and orthognathic management of a 14-year-old girl affected with Apert syndrome. She presented with a severe Class III skeletal relationship, midfacial hypoplasia and an large anterior open bite. Intraorally, she had severe crowding, a narrow maxilla and lateral posterior crossbites. The patient was treated with a combination of removable and fixed appliances, a transpalatal skeletal distractor and Le Fort I surgery. The extraoral characteristics improved and a good occlusal relationship between maxillary and mandibular teeth was achieved.

Published 22 June 2010 in J Orthod, 37(2): 121-7.
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